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قالب
:
انزيمات أيض الأحماض الأمينية
(تم التحويل من
قالب:Amino acid metabolism enzymes
)
v
t
e
أيض
:
أيض الأحماض الأمينية
-
synthesis
and catabolism
enzymes
(
essential
in CAPS)
K
→
acetyl-CoA
LYSINE
→
Saccharopine dehydrogenase
-
Glutaryl-CoA dehydrogenase
LEUCINE
→
Branched chain aminotransferase
-
Branched-chain alpha-keto acid dehydrogenase complex
-
Isovaleryl coenzyme A dehydrogenase
-
Methylcrotonyl-CoA carboxylase
-
Methylglutaconyl-CoA hydratase
-
3-hydroxy-3-methylglutaryl-CoA lyase
TRYPTOPHAN
→
Indoleamine 2,3-dioxygenase
/
Tryptophan 2,3-dioxygenase
-
Arylformamidase
-
Kynureninase
-
3-hydroxyanthranilate oxidase
-
Aminocarboxymuconate-semialdehyde decarboxylase
-
Aminomuconate-semialdehyde dehydrogenase
PHENYLALANINE
→
tyrosine
→
(see below)
G
→
pyruvate
glycine
→
serine
→
Serine hydroxymethyltransferase
-
Serine dehydratase
alanine
→
Alanine transaminase
cysteine
→
D-cysteine desulfhydrase
threonine
→
L-threonine dehydrogenase
G→
glutamate
HISTIDINE
→
Histidine ammonia-lyase
-
Urocanate hydratase
-
Formiminotransferase cyclodeaminase
proline
→
Proline oxidase
-
Pyrroline-5-carboxylate reductase
-
1-Pyrroline-5-carboxylate dehydrogenase
/
ALDH4A1
-
PYCR1
arginine
→
Ornithine aminotransferase
-
Ornithine decarboxylase
-
Agmatinase
→
alpha-ketoglutarate
→TCA
Glutamate dehydrogenase
G→
propionyl-CoA
VALINE
→
Branched chain aminotransferase
-
Branched-chain alpha-keto acid dehydrogenase complex
-
Enoyl-CoA hydratase
-
3-hydroxyisobutyryl-CoA hydrolase
-
3-hydroxyisobutyrate dehydrogenase
-
Methylmalonate semialdehyde dehydrogenase
ISOLEUCINE
→
Branched chain aminotransferase
-
Branched-chain alpha-keto acid dehydrogenase complex
-
3-hydroxy-2-methylbutyryl-CoA dehydrogenase
METHIONINE
→
Methionine adenosyltransferase
-
Adenosylhomocysteinase
-
Cystathionine beta synthase
-
Cystathionine gamma-lyase
(methionine synthesis:
MTR
/
Homocysteine methyltransferase
)
THREONINE
→
Threonine aldolase
→
succinyl-CoA
→TCA
Propionyl-CoA carboxylase
-
Methylmalonyl CoA epimerase
-
Methylmalonyl-CoA mutase
G→
fumarate
PHENYLALANINE
→
tyrosine
→
Phenylalanine hydroxylase
-
Tyrosine aminotransferase
-
4-Hydroxyphenylpyruvate dioxygenase
-
Homogentisate 1,2-dioxygenase
-
Fumarylacetoacetate hydrolase
G→
oxaloacetate
asparagine
→
aspartate
→
Asparaginase
/
Asparagine synthetase
-
Aspartate transaminase
Other
tyrosine
→
melanin
Tyrosinase
cysteine
+
glutamate
→
glutathione
Gamma-glutamylcysteine synthetase
-
Glutathione synthetase
-
Gamma-glutamyl transpeptidase
glycine
→
creatine
Guanidinoacetate N-methyltransferase
-
Creatine kinase
glutamate
→
glutamine
Glutamine synthetase
-
Glutaminase
proline
+
lysine
→
كولاجين
Prolyl hydroxylase
-
Lysyl hydroxylase
see also
disorders
,
intermediates
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